Li-11 DISEASES OF THE BILIARY SYSTEM by Dr. E. Orfei
Contents
Normal biliary tract ( See li-2-3)
li-11-1 Bilirubin Metabolism and disorders.
li-11-2 Bile acids metabolism and disorders.
CYSTIC DISORDERS
-Simple non-parasitic cysts
-Congenital polycystic disease
DILATATIONS
-Congenital hepatic fibrosis
-Caroli�s syndrome
ATRESIA
-Extrahepatic biliary atresia (EHBDA)
-Paucity of intrahepatic bile ducts, non syndromatic.
Byler's disease.
Noth american indian cholestasis.
Aagenaes syndrome (Hereditary cholestasis with lyphedema.)
- Paucity of intra-hepatic bile ducts, syndromatic.
Alagille syndrome
METABOLIC DEFECTS
Alpha-1-antitrypsin deficiency
Mucoviscidosis
Familial erythrophagocytic lymphohistiocytosis
li-11-4 Vanishing bile duct syndromes
IMMUNOLOGIC
Primary biliary cirrhosis.
Primary sclerosing cholangitis.
Graft versus host disease.
Hepatic allograft rejection.
Autoimmune cholangitis.
Sarcoidosis
TOXIC AND DRUG INDUCED
ISCHEMIC
INFECTIOUS
Bacterial.
Viral.
Protozoal.
NEOPLASTIC
Lymphoma.
Cholangiocarcinoma
Histiocytosis X
UNCLASSIFIED
Idiopathic adulthood ductopenia
li-11-5- Infections and infestations
Cholangitis, Cholangiolitis
li-11-6- Drug and toxic lesions
li-11-7- Cholelithiasis
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