Li-11 DISEASES OF THE BILIARY SYSTEM by Dr. E. Orfei
Contents
li-11- Normal biliary tract ( See li-2-3 )
li-11-1-Bilirubin metabolism (Physiology and Pathology)
li-11-2-Bile acids metabolism (Physiology and Pathology)
li-11-3 Developmental disorders of Bile Ducts
CYSTIC DISORDERS
-Simple non-parasitic cysts
-Congenital polycystic disease
DILATATIONS
-Congenital hepatic fibrosis
-Caroli�s syndrome
ATRESIA
-Extrahepatic biliary atresia (EHBDA)
-Paucity of intrahepatic bile ducts, non syndromatic( PIHBD)
Byler�s disease
North american indian cholestasis
Benign recurrent intrahepatic cholestasis
Metabolic defects
- Paucity of intra-hepatic bile ducts, syndromatic (SPIHBD)
Alagille syndrome
METABOLIC DIFECTS
Alpha-1-antitrypsin deficiency
Mucoviscidosis
Familial erythrophagocytic lymphohistiocytosis
li-11-4 Vanishing bile duct syndromes
IMMUNOLOGIC
-Primary biliary cirrhosis (PBC)
-Primary sclerosing cholangitis (PSC)
-Chronic graft -versus-host disease
-Hepatic allograft rejection
-Autoimmune cholangitis
-Sarcoidosis
TOXIC AND DRUG INDUCED
ISCHEMIC
INFECTIOUS
-Bacterial
-Viral
-Protozoal
NEOPLASTIC
-Lymphoma
-Cholangiocarcinama
-Histicytosis X
UNCLASSIFIED
-Idiopathic adulthood ductopenia
li-11-5- Infections and infestations
Cholangitis, Cholangiolitis
li-11-6- Drug and toxic lesions
li-11-7- Cholelithiasis
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